Cyclebase 3.0

Cell-cycle regulation database

COQ6 [YGR255C]

Flavin-dependent monooxygenase involved in ubiquinone biosynthesis; responsible for hydroxylation at position C5 and deamination at C4 during ubiquinone (Coenzyme Q) biosynthesis; localizes to matrix face of mitochondrial inner membrane in a large complex with other ubiquinone biosynthetic enzymes; human homolog COQ6 can complement yeast null mutant and is implicated in steroid-resistant nephrotic syndrome (SRNS); Belongs to the UbiH/COQ6 family.

Synonyms:  COQ6,  COQ6p,  P53318,  G9165,  P53318p ...

Linkouts:  STRING  UniProt